Shahin Abdollahifakhim
1 
, Faezeh Ghaderyan
1 , Hassan Soleimanpour
2* 1 Department of Otorhinolaryngology and Head and Neck Surgery, Faculty of Medicine, Tabriz University of Medical Sciences, Tabriz, Iran
2 Emergency and Trauma Care Research Center, Imam Reza General Hospital, Tabriz University of Medical Sciences, Tabriz, Iran
Abstract
Ankyloglossia superior (palatoglossal adhesion) is an exceedingly uncommon congenital disorder, with just 20 cases recorded in the medical literature. This abnormality is considered to be a part of the ankyloglossia superior syndrome (ASS) when it occurs with other congenital abnormalities such as gastrointestinal anomalies, cleft palate, and limb deformities. We describe the uncommon occurrence of a cleft palate, limb deformity, and ASS with a synechial band extending from the incisive foramen to the tip of the tongue. In addition, surgical repair is detailed. Considering the origin of ASS, we reviewed the current research and explored several hypotheses. When a newborn is diagnosed with ankyloglossia superior, clinicians must have a high level of suspicion for additional congenital defects.